Volume 4,Issue 5
IgA肾病合并Alport 综合征1例
IgA肾病（IgAN）是全球最常见的原发性肾小球疾病，也是终末期肾病的重要病因之一。Alport综合征（AS）为少见遗传性基底膜肾病，以血尿、肾功能进行性减退为主要表现。IgA肾病合并Alport综合征临床极为罕见，发病机制尚不明确，尚无统一规范的诊疗方案，患者总体预后欠佳。本文报道1例两种疾病共存的病例，结合临床、实验室及病理检查明确诊断，予针对性综合治疗。经长期规律随访，患者肾功能、尿蛋白等指标控制良好，病情稳定，为临床类似病例的早期识别、诊断与个体化治疗提供参考。
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